Pages that link to "Q36265198"
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The following pages link to Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy (Q36265198):
Displaying 50 items.
- Intraperoxisomal localization of very-long-chain fatty acyl-CoA synthetase: implication in X-adrenoleukodystrophy (Q22011096) (← links)
- Very long-chain acyl-CoA synthetases. Human "bubblegum" represents a new family of proteins capable of activating very long-chain fatty acids (Q24290132) (← links)
- Human peroxisomal 3-oxoacyl-coenzyme A thiolase deficiency (Q24293596) (← links)
- Molecular organization of peroxisomal enzymes: protein-protein interactions in the membrane and in the matrix (Q24294056) (← links)
- Putative X-linked adrenoleukodystrophy gene shares unexpected homology with ABC transporters (Q24321939) (← links)
- Distribution and cellular localization of adrenoleukodystrophy protein in human tissues: implications for X-linked adrenoleukodystrophy (Q24338719) (← links)
- Genetic heterogeneity in the cerebrohepatorenal (Zellweger) syndrome and other inherited disorders with a generalized impairment of peroxisomal functions. A study using complementation analysis (Q24561552) (← links)
- Large deletion of the peroxisomal acyl-CoA oxidase gene in pseudoneonatal adrenoleukodystrophy (Q24628708) (← links)
- Altered expression of ALDP in X-linked adrenoleukodystrophy (Q24671055) (← links)
- Progression of abnormalities in adrenomyeloneuropathy and neurologically asymptomatic X-linked adrenoleukodystrophy despite treatment with "Lorenzo's oil" (Q24673003) (← links)
- Fatty acid metabolism and the basis of brown adipose tissue function (Q26744147) (← links)
- Adrenoleukodystrophy: molecular genetics, pathology, and Lorenzo's oil (Q28270437) (← links)
- Accumulation of pristanic acid (2, 6, 10, 14 tetramethylpentadecanoic acid) in the plasma of patients with generalised peroxisomal dysfunction (Q28338863) (← links)
- Fatty acid composition of brain glycerophospholipids in peroxisomal disorders (Q28372514) (← links)
- Mouse very long-chain acyl-CoA synthetase in X-linked adrenoleukodystrophy (Q28507035) (← links)
- Functional Characterization of IPSC-Derived Brain Cells as a Model for X-Linked Adrenoleukodystrophy (Q28551048) (← links)
- Molecular cloning of cDNA encoding rat very long-chain acyl-CoA synthetase (Q28569176) (← links)
- Adrenoleukodystrophy and related disorders (Q30660504) (← links)
- Therapy of X-linked adrenoleukodystrophy (Q31034858) (← links)
- X-linked adrenoleukodystrophy: genes, mutations, and phenotypes (Q33607735) (← links)
- Peroxisomal disorders: clinical, biochemical, and molecular aspects (Q33607754) (← links)
- Adrenoleukodystrophy in a mother and son. (Q33629275) (← links)
- Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy (Q33655555) (← links)
- A missense point mutation (Ser515Phe) in the adrenoleukodystrophy gene in a family with adrenomyeloneuropathy: a clinical, biochemical, and genetic study (Q33733733) (← links)
- Biology of senescent liver peroxisomes: role in hepatocellular aging and disease (Q33742431) (← links)
- Impaired degradation of leukotrienes in patients with peroxisome deficiency disorders (Q33892786) (← links)
- Retinal very long-chain PUFAs: new insights from studies on ELOVL4 protein (Q33902007) (← links)
- Myelin and disorders that affect the formation and maintenance of this sheath (Q33971574) (← links)
- X-linked adrenoleukodystrophy. (Q34002811) (← links)
- Hydroxyeicosatetraenoic acid metabolism in cultured human skin fibroblasts. Evidence for peroxisomal beta-oxidation (Q34248207) (← links)
- Biochemistry of peroxisomes in health and disease (Q34418889) (← links)
- Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls (Q34488327) (← links)
- Peroxisomal bifunctional enzyme deficiency (Q34567743) (← links)
- Peroxisomal beta-oxidation enzyme proteins in adrenoleukodystrophy: distinction between X-linked adrenoleukodystrophy and neonatal adrenoleukodystrophy (Q34602966) (← links)
- Retroviral-mediated gene transfer corrects very-long-chain fatty acid metabolism in adrenoleukodystrophy fibroblasts (Q34644825) (← links)
- Histone deacetylase inhibitor upregulates peroxisomal fatty acid oxidation and inhibits apoptotic cell death in abcd1-deficient glial cells (Q34907267) (← links)
- A new peroxisomal disorder with enlarged peroxisomes and a specific deficiency of acyl-CoA oxidase (pseudo-neonatal adrenoleukodystrophy) (Q35245375) (← links)
- HDAC inhibitor SAHA normalizes the levels of VLCFAs in human skin fibroblasts from X-ALD patients and downregulates the expression of proinflammatory cytokines in Abcd1/2-silenced mouse astrocytes (Q35380239) (← links)
- ABCD1 deletion-induced mitochondrial dysfunction is corrected by SAHA: implication for adrenoleukodystrophy (Q35417932) (← links)
- Evaluation of therapy of X-linked adrenoleukodystrophy (Q35771255) (← links)
- Impaired mitochondrial fat oxidation induces adaptive remodeling of muscle metabolism (Q35796087) (← links)
- X-linked adrenoleukodystrophy: biochemical diagnosis and enzyme defect (Q35848817) (← links)
- Novel subtype of peroxisomal acyl-CoA oxidase deficiency and bifunctional enzyme deficiency with detectable enzyme protein: identification by means of complementation analysis (Q35888833) (← links)
- Lipid-lowering drugs (Q36002780) (← links)
- Ultrastructural and cytochemical demonstration of peroxisomes in cultured fibroblasts from patients with peroxisomal deficiency disorders (Q36213312) (← links)
- X linked adrenoleukodystrophy: clinical presentation, diagnosis, and therapy (Q36316914) (← links)
- The peroxisomal ABC transporter family (Q36622676) (← links)
- The peroxisome and the eye (Q36652090) (← links)
- Caffeic acid phenethyl ester induces adrenoleukodystrophy (Abcd2) gene in human X-ALD fibroblasts and inhibits the proinflammatory response in Abcd1/2 silenced mouse primary astrocytes (Q36713344) (← links)
- 25-hydroxycholesterol contributes to cerebral inflammation of X-linked adrenoleukodystrophy through activation of the NLRP3 inflammasome (Q37389923) (← links)