Vascular deficiency of Smad4 causes arteriovenous malformations: a mouse model of Hereditary Hemorrhagic Telangiectasia (Q49826259)

25 June 2018

title

Vascular deficiency of Smad4 causes arteriovenous malformations: a mouse model of Hereditary Hemorrhagic Telangiectasia (English)

1 reference

25 June 2018

hereditary hemorrhagic telangiectasia

main subject

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arteriovenous malformation

1 reference

Stryder M Meadows

5

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Angela M Crist

object named as

Angela M Crist

1

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author name string

Amanda R Lee

2

1 reference

25 June 2018

Nehal R Patel

3

1 reference

25 June 2018

Dawn E Westhoff

4

1 reference

25 June 2018

publication date

19 February 2018

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25 June 2018

published in

Angiogenesis

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25 June 2018

volume

21

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25 June 2018

issue

2

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25 June 2018

page(s)

363-380

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25 June 2018

Creative Commons Attribution 4.0 International

copyright license

start time

19 February 2018

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

describes a project that uses

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC5878194/fullTextXML

inferred from PubMed Central ID database lookup

cites work

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30 June 2018

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30 June 2018

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A murine model of hereditary hemorrhagic telangiectasia

30 June 2018

1 reference

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Defective angiogenesis in mice lacking endoglin

30 June 2018

1 reference

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30 June 2018

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Tacrolimus rescues the signaling and gene expression signature of endothelial ALK1 loss-of-function and improves HHT vascular pathology.

30 June 2018

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Endoglin prevents vascular malformation by regulating flow-induced cell migration and specification through VEGFR2 signalling

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Interaction Between ALK1 Signaling and Connexin40 in the Development of Arteriovenous Malformations.

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Executive summary of the 11th HHT international scientific conference

14 August 2018

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Bevacizumab in the treatment of hereditary hemorrhagic telangiectasia.

14 August 2018

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TGF-β signaling in development and disease

14 August 2018

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Endothelial Smad4 Maintains Cerebrovascular Integrity by Activating N-Cadherin through Cooperation with Notch

14 August 2018

1 reference

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Overlapping spectra of SMAD4 mutations in juvenile polyposis (JP) and JP-HHT syndrome.

14 August 2018

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Bevacizumab in hereditary hemorrhagic telangiectasia

14 August 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5878194

Arterial endothelium-specific activin receptor-like kinase 1 expression suggests its role in arterialization and vascular remodeling

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5878194

Cerebral vascular abnormalities in a murine model of hereditary hemorrhagic telangiectasia

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5878194

Genetic epidemiology of hereditary hemorrhagic telangiectasia in a local community in the northern part of Japan

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5878194

Endoglin expression in early development is associated with vasculogenesis and angiogenesis

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5878194

Abnormal pattern of Tie-2 and vascular endothelial growth factor receptor expression in human cerebral arteriovenous malformations

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5878194

Generation of Smad4/Dpc4 conditional knockout mice

14 August 2018

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12 December 2020

Genotype-phenotype correlation in hereditary hemorrhagic telangiectasia: mutations and manifestations

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12 December 2020

Life expectancy in patients with hereditary haemorrhagic telangiectasia

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12 December 2020

Pathogenesis of Arteriovenous Malformations in the Absence of Endoglin

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12 December 2020

10.1007/S10456-018-9602-0

Identifiers

DOI

1 reference

25 June 2018

PMC publication ID

5878194

1 reference

25 June 2018

PubMed publication ID

29460088

1 reference

25 June 2018