Protein folding stress in neurodegenerative diseases: a glimpse into the ER (Q37834769)

24 August 2017

1 reference

title

Protein folding stress in neurodegenerative diseases: a glimpse into the ER (English)

1 reference

https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

23 November 2024

0 references

1 reference

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A21288706

23 November 2024

2

Laurie H Glimcher

1 reference

24 August 2017

3

Claudio Hetz

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A21288706

23 November 2024

author name string

Soledad Matus

1

1 reference

24 August 2017

Laurie H. Glimcher

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A21288706

23 November 2024

language of work or name

English

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=21288706

23 November 2024

publication date

31 January 2011

1 reference

full work available at URL

24 August 2017

https://api.elsevier.com/content/article/PII:S0955067411000056?httpAccept=text/xml

1 reference

https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

https://api.elsevier.com/content/article/PII:S0955067411000056?httpAccept=text/plain

23 November 2024

1 reference

https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

Current Opinion in Cell Biology

23 November 2024

published in

1 reference

24 August 2017

volume

23

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24 August 2017

issue

2

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24 August 2017

page(s)

239-252

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Caspase-12 mediates endoplasmic-reticulum-specific apoptosis and cytotoxicity by amyloid-beta

24 August 2017

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Huntingtin has a membrane association signal that can modulate huntingtin aggregation, nuclear entry and toxicity

23 November 2024

127

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Huntingtin interacts with the cue domain of gp78 and inhibits gp78 binding to ubiquitin and p97/VCP.

23 November 2024

128

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Impaired ATF6α processing, decreased Rheb and neuronal cell cycle re-entry in Huntington's disease.

23 November 2024

129

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23 November 2024

Prions

130

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Subcellular colocalization of the cellular and scrapie prion proteins in caveolae-like membranous domains

23 November 2024

131

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Stressing out the ER: a role of the unfolded protein response in prion-related disorders

23 November 2024

132

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Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins

23 November 2024

133

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Gene expression profiling of the preclinical scrapie-infected hippocampus

23 November 2024

134

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Unfolded protein response transcription factor XBP-1 does not influence prion replication or pathogenesis.

23 November 2024

135

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Caspase-12 and endoplasmic reticulum stress mediate neurotoxicity of pathological prion protein.

23 November 2024

136

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The disulfide isomerase Grp58 is a protective factor against prion neurotoxicity.

23 November 2024

137

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Reduced translocation of nascent prion protein during ER stress contributes to neurodegeneration

23 November 2024

138

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Prion pathogenesis is independent of caspase-12.

23 November 2024

139

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Overexpressed protein disulfide isomerase in brains of patients with sporadic Creutzfeldt-Jakob disease

23 November 2024

140

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Human prion protein mutants with deleted and inserted octarepeats undergo different pathways to trigger cell apoptosis

23 November 2024

141

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Cellular tolerance of prion protein PrP in yeast involves proteolysis and the unfolded protein response

23 November 2024

142

1 reference

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Perturbation of endoplasmic reticulum homeostasis facilitates prion replication.

23 November 2024

143

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Conditions of endoplasmic reticulum stress favor the accumulation of cytosolic prion protein

23 November 2024

144

1 reference

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Conversion of PrP to a self-perpetuating PrPSc-like conformation in the cytosol

23 November 2024

145

1 reference

https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

Proteasomes and ubiquitin are involved in the turnover of the wild-type prion protein

23 November 2024

146

1 reference

https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

Alzheimer's disease: treatments in discovery and development

23 November 2024

147

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Soluble protein oligomers in neurodegeneration: lessons from the Alzheimer's amyloid beta-peptide

23 November 2024

148

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https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

Involvement of caspase-4 in endoplasmic reticulum stress-induced apoptosis and Abeta-induced cell death

23 November 2024

150

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https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

The unfolded protein response is activated in pretangle neurons in Alzheimer's disease hippocampus

23 November 2024

151

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The unfolded protein response is activated in Alzheimer's disease.

23 November 2024

152

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Rab6 is increased in Alzheimer's disease brain and correlates with endoplasmic reticulum stress

23 November 2024

153

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Protein disulfide isomerase-immunopositive inclusions in patients with Alzheimer disease

23 November 2024

154

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Induction of the unfolded protein response and cell death pathway in Alzheimer's disease, but not in aged Tg2576 mice

23 November 2024

155

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Increased Abeta1-42 production sensitizes neuroblastoma cells for ER stress toxicity

23 November 2024

156

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Abeta oligomers induce neuronal oxidative stress through an N-methyl-D-aspartate receptor-dependent mechanism that is blocked by the Alzheimer drug memantine

23 November 2024

157

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Involvement of endoplasmic reticulum Ca2+ release through ryanodine and inositol 1,4,5-triphosphate receptors in the neurotoxic effects induced by the amyloid-beta peptide.

23 November 2024

158

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Loss of HRD1-mediated protein degradation causes amyloid precursor protein accumulation and amyloid-beta generation

23 November 2024

159

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Comparative study of endoplasmic reticulum stress-induced neuronal death in rat cultured hippocampal and cerebellar granule neurons.

23 November 2024

160

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Activation of PERK signaling attenuates Abeta-mediated ER stress

23 November 2024

161

1 reference

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The E693Delta mutation in amyloid precursor protein increases intracellular accumulation of amyloid beta oligomers and causes endoplasmic reticulum stress-induced apoptosis in cultured cells

23 November 2024

162

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ER stress is involved in Abeta-induced GSK-3beta activation and tau phosphorylation

23 November 2024

163

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E2-25K/Hip-2 regulates caspase-12 in ER stress-mediated Abeta neurotoxicity

23 November 2024

164

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Phenylbutyric acid rescues endoplasmic reticulum stress-induced suppression of APP proteolysis and prevents apoptosis in neuronal cells

23 November 2024

165

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Lithium inhibits Abeta-induced stress in endoplasmic reticulum of rabbit hippocampus but does not prevent oxidative damage and tau phosphorylation

23 November 2024

166

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Toxicity mediated by soluble oligomers of beta-amyloid(1-42) on cholinergic SN56.B5.G4 cells

23 November 2024

167

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Abeta(1-42) and aluminum induce stress in the endoplasmic reticulum in rabbit hippocampus, involving nuclear translocation of gadd 153 and NF-kappaB.

23 November 2024

168

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GDNF regulates the A beta-induced endoplasmic reticulum stress response in rabbit hippocampus by inhibiting the activation of gadd 153 and the JNK and ERK kinases

23 November 2024

169

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Gene expression profile of the PDAPP mouse model for Alzheimer's disease with and without Apolipoprotein E.

23 November 2024

170

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GM1-ganglioside accumulation at the mitochondria-associated ER membranes links ER stress to Ca(2+)-dependent mitochondrial apoptosis

23 November 2024

171

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GM1-ganglioside-mediated activation of the unfolded protein response causes neuronal death in a neurodegenerative gangliosidosis

23 November 2024

172

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ER and oxidative stresses are common mediators of apoptosis in both neurodegenerative and non-neurodegenerative lysosomal storage disorders and are alleviated by chemical chaperones

23 November 2024

173

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Palmitoyl-protein thioesterase-1 deficiency mediates the activation of the unfolded protein response and neuronal apoptosis in INCL

23 November 2024

174

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No evidence for activation of the unfolded protein response in neuronopathic models of Gaucher disease

23 November 2024

175

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Lack of activation of the unfolded protein response in mouse and cellular models of Niemann-Pick type C disease.

23 November 2024

176

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Spinal cord trauma activates processing of xbp1 mRNA indicative of endoplasmic reticulum dysfunction.

23 November 2024

177

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Spinal cord injury induces endoplasmic reticulum stress with different cell-type dependent response

23 November 2024

178

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Stronger expression of CHOP and caspase 12 in diabetic spinal cord injury rats

23 November 2024

179

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Impact of the endoplasmic reticulum stress response in spinal cord after transient ischemia

23 November 2024

180

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Sodium 4-phenylbutyrate protects against spinal cord ischemia by inhibition of endoplasmic reticulum stress

23 November 2024

181

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https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

Endoplasmic reticulum stress in disorders of myelinating cells.

23 November 2024

182

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A little stress is good: IFN-gamma, demyelination, and multiple sclerosis.

23 November 2024

183

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Endoplasmic reticulum stress modulates the response of myelinating oligodendrocytes to the immune cytokine interferon-gamma

23 November 2024

184

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Interferon-gamma inhibits central nervous system remyelination through a process modulated by endoplasmic reticulum stress

23 November 2024

185

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Enhanced integrated stress response promotes myelinating oligodendrocyte survival in response to interferon-gamma

23 November 2024

186

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Increased Expression of Endoplasmic Reticulum Stress-Related Signaling Pathway Molecules in Multiple Sclerosis Lesions

23 November 2024

187

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Multiple sclerosis: risk factors, prodromes, and potential causal pathways

23 November 2024

188

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Ablation of the UPR-mediator CHOP restores motor function and reduces demyelination in Charcot-Marie-Tooth 1B mice

23 November 2024

189

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The unfolded protein response modulates disease severity in Pelizaeus-Merzbacher disease.

23 November 2024

190

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Heightened stress response in primary fibroblasts expressing mutant eIF2B genes from CACH/VWM leukodystrophy patients

23 November 2024

191

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A point mutation in translation initiation factor 2B leads to a continuous hyper stress state in oligodendroglial-derived cells

23 November 2024

192

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Restoration of visual function in P23H rhodopsin transgenic rats by gene delivery of BiP/Grp78

23 November 2024

193

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Suppression of retinal degeneration in Drosophila by stimulation of ER-associated degradation

23 November 2024

194

1 reference

https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

IRE1 signaling affects cell fate during the unfolded protein response

23 November 2024

195

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https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

ER stress protects from retinal degeneration

23 November 2024

196

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Unfolded protein response in a Drosophila model for retinal degeneration

23 November 2024

197

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Chemical chaperones protect from effects of apoptosis-inducing mutation in carbonic anhydrase IV identified in retinitis pigmentosa 17.

23 November 2024

198

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Pathogenesis of retinitis pigmentosa associated with apoptosis-inducing mutations in carbonic anhydrase IV.

23 November 2024

199

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Apoptosis-inducing signal sequence mutation in carbonic anhydrase IV identified in patients with the RP17 form of retinitis pigmentosa.

23 November 2024

200

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https://api.crossref.org/works/10.1016/J.CEB.2011.01.003

23 November 2024

Identifiers

1 reference

24 August 2017

1 reference