FUS Mislocalization and Vulnerability to DNA Damage in ALS Patients Derived hiPSCs and Aging Motoneurons. (Q37531676)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28082870%20AND%20SRC:MED&resulttype=core&format=json

9 April 2020

title

FUS Mislocalization and Vulnerability to DNA Damage in ALS Patients Derived hiPSCs and Aging Motoneurons (English)

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amyotrophic lateral sclerosis

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2

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Ann-Kathrin Huber

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Albert C Ludolph

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author name string

Julia Higelin

1

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Stefan Putz

3

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Jan P Delling

4

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Christian Jacob

5

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Anne-Kathrin Lutz

6

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Julia Bausinger

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Moritz Klingenstein

9

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Gotthold Barbi

10

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Günter Speit

11

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Annemarie Huebers

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Jochen H Weishaupt

13

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Andreas Hermann

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Stefan Liebau

15

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Tobias M Boeckers

17

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9 April 2020

publication date

26 December 2016

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Frontiers in Cellular Neuroscience

9 April 2020

published in

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volume

10

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page(s)

290

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describes a project that uses

9 April 2020

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8 June 2022

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ImageJ

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11 June 2022

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4-Aminopyridine Induced Activity Rescues Hypoexcitable Motor Neurons from Amyotrophic Lateral Sclerosis Patient-Derived Induced Pluripotent Stem Cells

6 September 2017

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A protein-protein interaction of stress-responsive myosin VI endowed to inhibit neural progenitor self-replication with RNA binding protein, TLS, in murine hippocampus.

14 September 2017

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14 September 2017

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14 September 2017

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Interaction of FUS and HDAC1 regulates DNA damage response and repair in neurons.

25 June 2018

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Requirements for stress granule recruitment of fused in sarcoma (FUS) and TAR DNA-binding protein of 43 kDa (TDP-43)

25 June 2018

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25 June 2018

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25 June 2018

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Developmental and Functional Nature of Human iPSC Derived Motoneurons

2 September 2018

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2 September 2018

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2 September 2018

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FUS-immunoreactive intranuclear inclusions in neurodegenerative disease.

2 September 2018

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Myosin-Va facilitates the accumulation of mRNA/protein complex in dendritic spines.

2 September 2018

1 reference

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The RNA binding protein TLS is translocated to dendritic spines by mGluR5 activation and regulates spine morphology.

2 September 2018

1 reference

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2 September 2018

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2 September 2018

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12 December 2020

An ALS-associated mutation in the FUS 3'-UTR disrupts a microRNA-FUS regulatory circuitry

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12 December 2020

TDP-43 and FUS: a nuclear affair

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12 December 2020

De novo FUS mutations are the most frequent genetic cause in early-onset German ALS patients

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12 December 2020

Identifiers

DOI

10.3389/FNCEL.2016.00290

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28082870%20AND%20SRC:MED&resulttype=core&format=json

9 April 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28082870%20AND%20SRC:MED&resulttype=core&format=json

9 April 2020

PubMed publication ID

28082870

1 reference