Mitochondrial Lon protease in human disease and aging: Including an etiologic classification of Lon-related diseases and disorders (Q28071866)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

review article

1 reference

title

Mitochondrial Lon protease in human disease and aging: Including an etiologic classification of Lon-related diseases and disorders (English)

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

author name string

Daniela A Bota

series ordinal

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

language of work or name

1 reference

5 July 2016

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

Free Radical Biology and Medicine

17 March 2020

published in

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

volume

100

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

page(s)

188-198

2 references

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PINK1-Parkin pathway activity is regulated by degradation of PINK1 in the mitochondrial matrix

17 March 2020

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StAR enhances transcription of genes encoding the mitochondrial proteases involved in its own degradation

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20 March 2017

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Enhanced mitochondrial biogenesis is associated with increased expression of the mitochondrial ATP-dependent Lon protease

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29 September 2017

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Upregulation of the mitochondrial Lon Protease allows adaptation to acute oxidative stress but dysregulation is associated with chronic stress, disease, and aging.

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2 June 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Turnover and transformation of mitochondrial acetyl-CoA acetyltransferase into CoA-modified forms

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Purification and characterization of a substrate protein for mitochondrial ATP-dependent protease in bovine adrenal cortex

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Newly recognized syndrome of cerebral, ocular, dental, auricular, skeletal anomalies: CODAS syndrome--a case report

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Mitochondrial Lon protease controls ROS-dependent apoptosis in cardiomyocyte under hypoxia.

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

ATP-Dependent Lon Protease Controls Tumor Bioenergetics by Reprogramming Mitochondrial Activity

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Oxidative post-translational modifications develop LONP1 dysfunction in pressure overload heart failure

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Protective role of the mitochondrial Lon protease 1 in ochratoxin A-induced cytotoxicity in HEK293 cells.

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Frataxin deficiency causes upregulation of mitochondrial Lon and ClpP proteases and severe loss of mitochondrial Fe-S proteins

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Transcriptional regulation of the cholesterol side chain cleavage cytochrome P450 gene (CYP11A1) revisited: binding of GATA, cyclic adenosine 3',5'-monophosphate response element-binding protein and activating protein (AP)-1 proteins to a distal nov

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Nucleotide sequence for cDNA of bovine mitochondrial ATP-dependent protease and determination of N-terminus of the mature enzyme from the adrenal cortex

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Mitochondrial transcription factor A regulates mtDNA copy number in mammals

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Modulation of Lon protease activity and aconitase turnover during aging and oxidative stress.

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Critical roles of AMP-activated protein kinase in constitutive tolerance of cancer cells to nutrient deprivation and tumor formation

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Substitution of PIM1 protease in mitochondria by Escherichia coli Lon protease.

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5183306

Mitochondrial genetics and disease

27 November 2018

1 reference

12 December 2020

Mitochondrial adaptations in skeletal muscle to hindlimb unloading

1 reference

12 December 2020

Mutations inLONP1, a mitochondrial matrix protease, cause CODAS syndrome

1 reference

12 December 2020

In vitro degradation of mitochondrial proteins by ATP-dependent protease in bovine adrenal cortex

1 reference

12 December 2020

An iTRAQ-based mitoproteomics approach for profiling the nephrotoxicity mechanisms of ochratoxin A in HEK 293 cells

1 reference

12 December 2020

ATP-dependent protease in human placenta

1 reference

12 December 2020

Expression of nuclear-encoded genes involved in mitochondrial biogenesis and dynamics in experimentally denervated muscle

1 reference

12 December 2020

Muscle regeneration occurs to coincide with mitochondrial biogenesis

1 reference

12 December 2020

ATP-dependent protease in bovine adrenal cortex. Tissue specificity, subcellular localization, and partial characterization

1 reference

12 December 2020

Commentary on "Downregulation of the human Lon protease impairs mitochondrial structure and function and causes cell death" by D.A. Bota, J.K. Ngo, and K.J.A. Davies

1 reference

12 December 2020

Adrenal cortex mitochondrial enzyme with ATP-dependent protease and protein-dependent ATPase activities. Purification and properties

1 reference

12 December 2020

10.1016/J.FREERADBIOMED.2016.06.031

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27387767%20AND%20SRC:MED&resulttype=core&format=json

17 March 2020

PubMed publication ID

2 references