Cell-autonomous death of cerebellar purkinje neurons with autophagy in Niemann-Pick type C disease (Q24811579)

2

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Steven M Beier

3

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Hermogenes Manuel

4

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JoAnn Buchanan

5

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Matthew P Scott

Creative Commons Attribution 4.0 International

6

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language of work or name

English

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publication date

July 2005

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published in

PLOS Genetics

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volume

1

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issue

1

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page(s)

81-95

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copyright license

start time

25 July 2005

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

describes a project that uses

ImageJ

1 reference

Europe PubMed Central

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC1183526/fullTextXML

inferred from PubMed Central ID database lookup

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Neurons in Niemann-Pick disease type C accumulate gangliosides as well as unesterified cholesterol and undergo dendritic and axonal alterations

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30 May 2018

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30 May 2018

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30 May 2018

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Apoptosis accompanied by up-regulation of TNF-alpha death pathway genes in the brain of Niemann-Pick type C disease

30 May 2018

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28 November 2018

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Niemann-Pick type C disease involves disrupted neurosteroidogenesis and responds to allopregnanolone

28 November 2018

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Axonal dystrophy of dorsal root ganglion sensory neurons in a mouse model of Niemann-Pick disease type C.

28 November 2018

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A relationship between cerebellar Purkinje cells and spatial working memory demonstrated in a lurcher/chimera mouse model system

28 November 2018

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Microglia promote the death of developing Purkinje cells

28 November 2018

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28 November 2018

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Wild-Type Nonneuronal Cells Extend Survival of SOD1 Mutant Motor Neurons in ALS Mice

28 November 2018

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Sprouting of adult Purkinje cell axons in lesioned mouse cerebellum: "non-permissive" versus "permissive" environment

28 November 2018

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28 November 2018

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28 November 2018

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Rescue of neurodegeneration in Niemann-Pick C mice by a prion-promoter-driven Npc1 cDNA transgene

28 November 2018

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Cytotoxic Effect of Brain Macrophages on Developing

28 November 2018

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Neuronal alpha-synucleinopathy with severe movement disorder in mice expressing A53T human alpha-synuclein

28 November 2018

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Cognitive deficit and development of motor impairment in a mouse model of Niemann-Pick type C disease

28 November 2018

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Neurodegeneration in Niemann-Pick type C disease mice

28 November 2018

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CNS synaptogenesis promoted by glia-derived cholesterol

28 November 2018

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A subset of NSAIDs lower amyloidogenic Abeta42 independently of cyclooxygenase activity

28 November 2018

1 reference

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Degeneration of neurons and glia in the Niemann-Pick C mouse is unrelated to the low-density lipoprotein receptor

28 November 2018

1 reference

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Regional and developmental expression of the Npc1 mRNA in the mouse brain.

28 November 2018

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Embryonic Striatal Neurons from Niemann-Pick Type C Mice Exhibit Defects in Cholesterol Metabolism and Neurotrophin Responsiveness

28 November 2018

1 reference

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GABAergic neuroaxonal dystrophy and other cytopathological alterations in feline Niemann-Pick disease type C

28 November 2018

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Cerebellar degeneration in the Niemann-Pick type C mouse

28 November 2018

1 reference

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Sphingomyelinosis, a new mutation in the mouse: a model of Niemann-Pick disease in humans

28 November 2018

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Interaction of granule, Purkinje and inferior olivary neurons in lurcher chimaeric mice. I. Qualitative studies.

28 November 2018

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Cerebellar involvement in murine sphingomyelinosis: a new model of Niemann-Pick disease

28 November 2018

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12 December 2020

Low density lipoprotein (LDL)-mediated suppression of cholesterol synthesis and LDL uptake is defective in Niemann-Pick type C fibroblasts

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12 December 2020

Neurodegeneration in the Niemann-Pick C mouse: glial involvement

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12 December 2020

A lysosomal storage disorder in mice characterized by a dual deficiency of sphingomyelinase and glucocerebrosidase

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12 December 2020

Alleviation of neuronal ganglioside storage does not improve the clinical course of the Niemann-Pick C disease mouse

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12 December 2020

Lysosomal storage diseases

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12 December 2020

Microglial tissue plasminogen activator (tPA) triggers neuronal apoptosis in vitro

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12 December 2020

Lack of Purkinje cell loss in adult rat cerebellum following protracted axotomy: Degenerative changes and regenerative attempts of the severed axons

1 reference

12 December 2020

10.1371/JOURNAL.PGEN.0010007

Identifiers

DOI

1 reference

1 reference

1 reference

PubMed publication ID

16103921

1 reference