Congenital Cataract
Congenital Cataract
Congenital Cataract
Patients Data
y A. G. y 4 months old y Female y Filipino y Resides in Marikina y Roman Catholic y Mother:
60% Reliable
Chief Complaint:
s/p Lensectomy of OD
ADMISSION
Birth History
y Born Full Term to a G3P3 (3003) mother y Delivered via NSD in a lying in and assissted by a
midwife and OB-Gyne y Birthweight = 7.2 lbs y Mother had a total of 12 prenatal check-ups in a private clinic y Mother had an asthma attack on her 8th month of pregnancy
Family History
y Cataract Maternal Grandfather Senile mature cataract Paternal Uncle
supervisors y Is usually left at home with aunt when parents are at work
Immunization History
Physical Examination
AT THE OPD JULY 28, 2010
Vital Signs
y Heart Rate y Respiratory Rate y Temperature
Eye Examination
y Gross Examination Eye position symmetric. Lids
OU
Lashes
OU
Eye Examination
y Gross Examination
Conjunctiva. OU - No swollen glands. Bulbar conjunctiva clear. Palpebral conjunctiva pink. Scleara OU Unicteric Cornea. OU - Cornea clear with no lesions, opacities, mass. Anterior chamber. OU - formed and clear. Pupils OU - Pupils are symmetric and round, measure 3 mm, equally brisk and reactive to light.
Eye Examination
y Extra Ocular Muscles
Eye Examination
y Tonometry
Unremarkable
y Ophthalmoscopy.
OD
dull red orange reflex. Clear media with peripheral opacity
Slightly
OS
Very
Cup disk ratio and macula were not appreciated because of the dull red orange reflexes and cloudy media.
(Ophthalmic)
Difficulty to assess optic disc, retina on fundoscopy Sensitive to light source in a dark room With visual fixation Pupils equal, 2-3mm, EBRTL | partial ROR, OU
y III
(Oculomotor)
No ptosis, outward, downward, adduction or elevation displacements of both eyes Intact EOMs
(Trigeminal)
Corneal response in both eyes
Salient Features
History Physical Exam
difficult
Differentials
y Retinoblastoma y Congenital Cataract
Admitting Diagnosis
SENILE MATURE CATARACT, OS
Day 1
1 drop Q4
Day 2
y Subjective Irritable when wearing the eye patch y Objective Unremarkable findings on general physical examination
y Assessment Congenital Cataract, OS s/p Lensectomy with partial vitrectomy OU y Plan Moxifloxacin eye drops
y Subjective Better activity Left eye now able to see light and follow objects y Objective Otherwise unremarkable findings
Operative technique
y Patient Supine y Anesthesia inducted y Asepsis and antisepsis y Sterile drapes placed y Lid retractors placed y Stab incision at 2 o clock position y Intracaneral tryphan blue y Irrigation of tryphan blue
Operative technique
y Intracaneral OVD y Main port incision at 10 o clock position y Anterior capsulotomy y I and A of lens material y Part anterior chamber vitrectomy y Final I and A y Suturing with nylon 10-0 (corneal suture) y Eye patching
V 11 H 11 8.5 10.0
OS:
OS:
Day 3
y Assessment Congenital Cataract, OS s/p Lensectomy with partial vitrectomy OU y Plan Moxifloxacin eye drops
Advised
y Follow-up y Wearing of protective eye patch y Compliance to medications y Watch out for postoperative complications, consult
should be done
Congenital Cataract
y Congenital (infantile) cataracts Present at birth or appear shortly thereafter May be unilateral or bilateral y About one-third of cataracts are hereditary y Another third are secondary to metabolic or
infectious diseases or associated with a variety of syndromes. y The final one-third result from undetermined causes.
Congenital Cataract
y Congenital lens opacities are common and often
visually insignificant. y A partial opacification or one out of the visual axisor not dense enough to interfere significantly with light transmissionrequires no treatment. y Dense central congenital cataracts require surgery.
Congenital Cataract
y Congenital cataracts that cause significant visual loss y y
y y
must be detected early Large, dense white cataracts may present as leukocoria (white pupil), noticeable by the parents, Unilateral infantile cataracts that are dense, central, and larger than 2 mm,will cause permanent amblyopia if not treated within the first 2 months of life. Symmetric (equally dense) bilateral cataracts may require less urgent management. When surgery is undertaken, there must be as short an interval as is reasonably possible between surgery on the two eyes.
Congenital Cataract
y Lens extraction through a small limbal incision
utilizing a mechanical irrigation aspiration handpiece. y Phacoemulsification is rarely required. y The posterior capsule and anterior vitreous are removed using a mechanical vitreous suction-cutting instrument.
Prevents formation of secondary capsular opacification or after-cataract Avoids the necessity for secondary surgery and enhances early optical correction.
Congenital Cataract
y Complications are similar to those reported with
adult cataract procedures. y Optical correction can consist of spectacles in older bilaterally aphakic children y Most childhood cataract operations are followed by contact lens correction y Use of intraocular lenses in early childhood is becoming increasingly frequent. I
Lessens the difficulty of optical rehabilitation associated with contact lenses in children May need to be changed as the eye develops.
Congenital Cataract
y The visual prognosis for childhood cataract patients
requiring surgery is not as good as age-related cataract. y Amblyopia and occasional anomalies of the optic nerve or retina limit the degree of useful vision that can be achieved. y The prognosis for improvement of visual acuity is worst following surgery for unilateral congenital cataracts and best for incomplete bilateral congenital cataracts that are slowly progressive.