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    Everything You Need To Know and More

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    Bridget Mullins
    Cystic fibrosis is a genetic disorder that causes thick mucus buildup in the lungs and digestive tract, leading to organ damage. It most commonly affects Caucasians and is usually diagnosed at birth. Common symptoms include salty-tasting skin, coughing, and poor weight gain. Treatment involves chest physical therapy, antibiotics, enzymes to aid digestion, and other medications administered via nebulizer. Proper handwashing and avoiding infection are important interventions for managing the condition.

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    Everything You Need To Know and More

    Uploaded by

    Bridget Mullins
    21 views15 pages
    Cystic fibrosis is a genetic disorder that causes thick mucus buildup in the lungs and digestive tract, leading to organ damage. It most commonly affects Caucasians and is usually diagnosed at birth. Common symptoms include salty-tasting skin, coughing, and poor weight gain. Treatment involves chest physical therapy, antibiotics, enzymes to aid digestion, and other medications administered via nebulizer. Proper handwashing and avoiding infection are important interventions for managing the condition.

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    Cystic Fibrosissss

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    Cystic fibrosis is a genetic disorder that causes thick mucus buildup in the lungs and digestive tract, leading to organ damage. It most commonly affects Caucasians and is usually diagnosed at birth. Common symptoms include salty-tasting skin, coughing, and poor weight gain. Treatment involves chest physical therapy, antibiotics, enzymes to aid digestion, and other medications administered via nebulizer. Proper handwashing and avoiding infection are important interventions for managing the condition.

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    Attribution Non-Commercial (BY-NC)
    Download as PPT, PDF, TXT or read online from Scribd
    Download as ppt, pdf, or txt
    21 views15 pages

    Everything You Need To Know and More

    Uploaded by

    Bridget Mullins
    Cystic fibrosis is a genetic disorder that causes thick mucus buildup in the lungs and digestive tract, leading to organ damage. It most commonly affects Caucasians and is usually diagnosed at birth. Common symptoms include salty-tasting skin, coughing, and poor weight gain. Treatment involves chest physical therapy, antibiotics, enzymes to aid digestion, and other medications administered via nebulizer. Proper handwashing and avoiding infection are important interventions for managing the condition.

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    Some schools do not have a full time nurse
    Full time school nurses may not always be available
    It is estimated that 30,000 people have cystic fibrosis
    in the US
    What is Cystic Fibrosis
    CDC defines cystic fibrosis as an genetically inherited
    disease that results in organ failure in the respiratory,
    gastric, and other sites.
    Cystic fibrosis is the most common genetic disorder
    in children.
    Cystic fibrosis is most common in Caucasians but
    affects all races.
    Cystic fibrosis is usually diagnosed at birth and the
    mean age of survival is 37.4.
    Symptoms of Cystic Fibrosis
     “Salty” tasting skin
     Bloody sputum (spit)
     Thick, sticky mucous
     Diarrhea
     Foul smelling stools
     Stomach pain
     Poor weight gain and growth
     Constipation
     Frequent coughing
     Tiredness/weakness
     Fever
     Note: Make sure you tell the child to alert you of any of the above symptoms
    because interventions need to be taken. An intervention such as medication
    administration would alleviate most of the symptoms experienced.
    Interventions for the child with
    Cystic Fibrosis
    For frequent coughing- this could be disruptive to
    classmates therefore an intervention would be to sit the
    child next to the door in order for them to step out if need
    be. Also assign another classmate to go with them to
    monitor the student and seek help if further intervention
    is needed.
    Note for dehydration-allow student to have sports bottle
    with appropriate beverage in the classroom.  This is also
    important is keeping secretions thin.
    Tiredness/weakness- this is common in long hour school
    days therefore an intervention would be to allow the child
    frequent rest periods during school days to account for the
    fatigue.
    Factors that can trigger outbreaks
    of Cystic Fibrosis
    Smoking
    Stress
    Dehydration
    Infection
    Fear
    Anxiety
    Depression
    Interventions for the child with
    Cystic Fibrosis
    To prevent infections-sure that the child washes their hands
    after going to the bathroom and before eating. This is going to
    be essential in preventing infection.
    For the child experiencing an active infection-place the child’s
    desk away from any sick kids that are in the classroom to try to
    prevent any unnecessary infections. Again hand washing is
    essential in preventing the spread of infections throughout your
    classroom.
    If the child is expressing fear, anxiety, or depression-with the
    above symptoms tell the child that if they experience any of
    these symptoms there is a guidance counselor at most schools
    that they can talk to throughout their day to alleviate these
    feelings. If a guidance counselor is not present question why
    they are feeling like this and try to counsel the child.
    Handwashing
    Wash your hands, and suggest hand washing to
    PREVENT infection
    Wet hands with warm water
    Apply hand wash or soap
    Lather and wash for at LEAST 15 seconds and scrub
    fingernails onto palms
    Rinse both sides of hands with water
    Dry hands and shut off faucet with towel
    Important Facts
    Symptoms vary from person to person and vary
    overtime.
    CF can cause severe breathing problems which can
    result in permanent lung damage
    CF affects almost all organs of the body
    CF has NO cure, but treatment is improving
    Common Treatment Plan
    Chest physical therapy-to cough up secretions
    Antibiotics to treat infections.
    Anti-inflammatory medications to reduce swelling in
    your airway
    Bronchodilator medications-open up airways
    Pancreatic Enzymes- to be able to digest fats and
    proteins
    High Calorie Shakes- for poor nutrition and growth
    Supplements- for vitamin deficiency.
    Common medications for Cystic
    Fibrosis
    Tobi –inhaled medication through a nebulizer ,
    usually taken every 12 hours and stored in a
    refrigerator and in a dark room
    Side effects that are NORMAL-sore throat, headache,
    unpleasant taste in mouth, hoarseness
    WARNING if seeing these side effects alert someone-
    coughing, wheezing, shortness of breath
    Common medications for Cystic
    Fibrosis
    Pulmozyme- inhaled medication through a nebulizer
    that is used to break up mucous usually taken once a
    day and stored in a refridgerator
    Side Effects that are NORMAL-Changes in voice, sore
    throat, stuffy or runny nose, dizziness, eye irritation,
    rash
    WARNING if seeing these side effects alert someone-
    trouble breathing, hives, swelling of throat, chest pain
    Common medications for Cystic
    Fibrosis
    Pancreatic Enzymes (Pancrease, Pancreacarb, Ultrase, Creon)-
    aid in digestion of fats, carbohydrates, and proteins.
    Should be taken before meals and snacks
    Note: If taking multiple enzymes take some before the meal and
    the rest at various points throughout the meal.
    SHOULD NOT chew or crush
    Comes in powder, capsule, or tablet
    Should NEVER be stored in refrigerator
    Side Effects that are NORMAL-nausea, vomiting, diarrhea,
    cramping, constipation, bloating
    WARNING if seeing these side effects alert someone-black tarry
    stools, bloody diarrhea, pain or swelling in joints
    Common medications for Cystic
    Fibrosis
    Azithromycin- antibiotic to treat a certain type of
    bacteria called P. Aeuroginosa that causes infections
    Can be taken orally, tablet, or liquid suspension
    Usually taken 3X a week
    Should be stored at room temperature
    NORMAL side effects- nausea, diarrhea, abdominal
    pain, unpleasant taste in mouth, headache, dizziness
    WARNING if seeing these side effects alert someone-
    bloody diarrhea, swelling of face, chest pain, rash,
    yellowing of skin
    References
    http://www.nhlbi.nih.gov/health/dci/Diseases/cf/cf_treatm
    ents.html
    www.cdc.gov/
    Moore, C.E. (2006).  Cystic Fibrosis.  In J. Selekman
    (Ed.), School nursing: A comprehensive text.  (pp. 747-
    756).  Philadelphia, PA: F.A. Davis Company.
    Skidmore-Roth, Linda Mosby's Nursing Drug Reference.
    St. Louis : Mosby, 2009 (ref RM138 .S59 2009)

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