(Q41180881)

27 September 2017

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title

Neuropathology and pathogenesis of mitochondrial diseases (English)

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27 September 2017

G K Brown

1

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27 September 2017

M V Squier

series ordinal

2

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27 September 2017

publication date

1 January 1996

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Journal of Inherited Metabolic Disease

27 September 2017

published in

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27 September 2017

volume

19

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27 September 2017

issue

4

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27 September 2017

page(s)

553-572

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Alternative excitotoxic hypotheses

27 September 2017

cites work

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Electrophysiological properties of rat CA1 pyramidal neurones in vitro modified by changes in extracellular bicarbonate

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

The effects of extracellular acidosis on neurons and glia in vitro

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Familial poliodystrophy, mitochondrial myopathy, and lactate acidemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Hydrogen ions kill brain at concentrations reached in ischemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Mitochondrial encephalomyopathy with lactate-pyruvate elevation and brain infarctions

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

What causes infarction in ischemic brain?: The Robert Wartenberg Lecture

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Familial poliodystrophy, mitochondrial myopathy, and lactate acidemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Ion homeostasis in rat brain in vivo: intra- and extracellular [Ca2+] and [H+] in the hippocampus during recovery from short-term, transient ischemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Brain lactic acidosis and synaptic function

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FBF01799116

Neurotoxicity at the N-methyl-D-aspartate receptor in energy-compromised neurons. An hypothesis for cell death in aging and disease.

21 January 2018

1 reference

12 December 2020

Mitochondrial encephalomyopathies: a correlation between neuropathological findings and defects in mitochondrial DNA.

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12 December 2020

Pyruvate dehydrogenase complex deficiency as a cause of subacute necrotizing encephalopathy (Leigh disease).

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12 December 2020

Brain extracellular ion composition and EEG activity following 10 minutes ischemia in normo- and hyperglycemic rats

1 reference

12 December 2020

Biochemical and histologic pathology in an infant with cross-reacting material (negative) pyruvate carboxylase deficiency

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12 December 2020

Astrocytes: form, functions, and roles in disease

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12 December 2020

Acidosis and ischemic brain damage.

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12 December 2020

Evolving concepts about the role of acidosis in ischemic neuropathology

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12 December 2020

Nitric oxide mediates angiogenesis in vivo and endothelial cell growth and migration in vitro promoted by substance P.

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12 December 2020

Status spongiosus of nervous tissue. Electron microscopic studies

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12 December 2020

Transient focal ischemia in hyperglycemic rats is associated with increased cerebral infarction

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12 December 2020

Pyruvate dehydrogenase deficiency

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12 December 2020

[An autopsy case of degenerative type myoclonus epilepsy associated with Friedreich's ataxia and mitochondrial myopathy (author's transl)]

1 reference

12 December 2020

2,3-Dihydroxy-6-nitro-7-sulfamoyl-benzo(F)quinoxaline: a neuroprotectant for cerebral ischemia

1 reference

12 December 2020

Hypoxic stimulation of vascular endothelial growth factor expression in vitro and in vivo.

1 reference

12 December 2020

Relations between postmortem alterations and glycolytic metabolism in the brain

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12 December 2020

Oxygen radical mechanisms of brain injury following ischemia and reperfusion

1 reference

12 December 2020

Myoclonus, cerebellar disorder, neuropathy, mitochondria1 myopathy, and ACTH deficiency

1 reference

12 December 2020

Myoclonus epilepsy associated with ragged-red fibres (mitochondrial abnormalities ): disease entity or a syndrome? Light-and electron-microscopic studies of two cases and review of literature

1 reference

12 December 2020

Functional/metabolic modulation of the brain stem lesions caused by 1,3-dinitrobenzene in the rat

1 reference

12 December 2020

Antidiabetic sulfonylureas: localization of binding sites in the brain and effects on the hyperpolarization induced by anoxia in hippocampal slices.

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12 December 2020

Pathogenic factors underlying the lesions in Leigh's disease. Tissue responses to cellular energy deprivation and their clinico-pathological consequences

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12 December 2020

Neuropathology of mitochondrial encephalomyopathies due to mitochondrial DNA defects.

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12 December 2020

Cytochrome c oxidase-associated Leigh syndrome: Phenotypic features and pathogenetic speculations

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12 December 2020

A fourth case of fumarase deficiency

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12 December 2020

Mechanisms of blockade of excitatory amino acid receptor channels

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12 December 2020

Neuropathology in cerebral lactic acidosis

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12 December 2020

Isolated capillary proliferation in Leigh's syndrome

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12 December 2020

Selective vulnerability of the hippocampus to ischemia--reversible and irreversible types of ischemic cell damage

1 reference

12 December 2020

Myoclonus epilepsy and ragged-red fibres (MERRF). 1. A clinical, pathological, biochemical, magnetic resonance spectrographic and positron emission tomographic study

1 reference

12 December 2020

Arachidonic acid in the modulation of excitable membrane function and at the onset of brain damage

1 reference

12 December 2020

Clinical presentation of mitochondrial respiratory chain defects in NADH-coenzyme Q reductase and cytochrome oxidase: clues to pathogenesis of Leigh disease

1 reference

12 December 2020

Myoclonic epilepsy and ragged-red fibers with cytochrome oxidase deficiency: neuropathology, biochemistry, and molecular genetics

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12 December 2020

Neuropathology in Kearns-Sayre syndrome

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12 December 2020

Central nervous system changes in mitochondrial encephalomyopathy: light and electron microscopic study

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12 December 2020

Proton inhibition of N-methyl-D-aspartate receptors in cerebellar neurons

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12 December 2020

Mitochondrial encephalomyopathy (MELAS): pathological study and successful therapy with coenzyme Q10 and idebenone

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12 December 2020

Calcium-mediated neurotoxicity: relationship to specific channel types and role in ischemic damage

1 reference

12 December 2020

Neuropathology of myoclonus epilepsy associated with ragged-red fibers (Fukuhara's disease).

1 reference

12 December 2020

Astrocytic swelling due to hypotonic or high K+ medium causes inhibition of glutamate and aspartate uptake and increases their release

1 reference

12 December 2020

The development of mitochondrial medicine

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12 December 2020

Mitochondrial angiopathy in cerebral blood vessels of mitochondrial encephalomyopathy

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12 December 2020

"Swayback": A Congenital Demyelinating Disease of Lambs with Affinities to Schilder's Encephalitis: (Section of Comparative Medicine).

1 reference

12 December 2020

Neonatal congenital lactic acidosis with pyruvate carboxylase deficiency in two siblings

1 reference

12 December 2020

An autopsy case of mitochondrial encephalomyopathy: biochemical and electron microscopic studies of the brain.

1 reference

12 December 2020

Biotinidase deficiency: a cause of subacute necrotizing encephalomyelopathy (Leigh syndrome). Report of a case with lethal outcome

1 reference

12 December 2020

Molecular diversity of glutamate receptors and implications for brain function

1 reference

12 December 2020

Mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes with acanthocytosis: a clinicopathological study of a unique case

1 reference

12 December 2020

Apoptosis and necrosis: two distinct events induced, respectively, by mild and intense insults with N-methyl-D-aspartate or nitric oxide/superoxide in cortical cell cultures

1 reference

12 December 2020

Juvenile form of spongy degeneration of the CNS.

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12 December 2020

Modulation of the N-methyl-D-aspartate channel by extracellular H+

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12 December 2020

Spongiform encephalopathy with chronic progressive external ophthalmoplegia. Central ophthalmoplegia mimicking ocular myopathy

1 reference

12 December 2020

Hyperpolarizing vasodilators activate ATP-sensitive K+ channels in arterial smooth muscle

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12 December 2020

The pathophysiology of brain ischemia

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12 December 2020

The Development of Enzymes of Energy Metabolism in the Brain of a Precocial (Guinea Pig) and Non-Precocial (Rat) Species

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12 December 2020

Selective vulnerability in acute energy deprivation syndromes

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12 December 2020

Characterization of the mutations in three patients with pyruvate dehydrogenase E1 alpha deficiency

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12 December 2020

Cytotoxic effects of acidic and sulphur containing amino acids on the infant mouse central nervous system

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12 December 2020

Cerebral infarction. Evolution of histopathological changes after occlusion of a middle cerebral artery in primates

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12 December 2020

Cerebral hypoxia: some new approaches and unanswered questions

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12 December 2020

The mutation at nt 8993 of mitochondrial DNA is a common cause of Leigh's syndrome

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12 December 2020

Glutamate, nitric oxide and cell-cell signalling in the nervous system

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12 December 2020

Adenosine 5'-triphosphate-sensitive potassium channels

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12 December 2020

Identifiers

DOI

10.1007/BF01799116

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Dimensions Publication ID

27 September 2017

1005901360

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