(Q38349291)

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Mannose 6-phosphate receptor-mediated uptake is defective in acid sphingomyelinase-deficient macrophages: implications for Niemann-Pick disease enzyme replacement therapy

scientific article published on 13 October 2003

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scholarly article

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

Mannose 6-phosphate receptor-mediated uptake is defective in acid sphingomyelinase-deficient macrophages: implications for Niemann-Pick disease enzyme replacement therapy (English)

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

enzyme replacement therapy

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Niemann-Pick disease

1 reference

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inferred from title

Edward H Schuchman

2

object named as

Edward H Schuchman

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

author name string

Rajwinder Dhami

1

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

language of work or name

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publication date

13 October 2003

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Europe PubMed Central

PubMed publication ID

2 September 2017

Journal of Biological Chemistry

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Europe PubMed Central

PubMed publication ID

2 September 2017

279

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Europe PubMed Central

PubMed publication ID

2 September 2017

2

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

1526-1532

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

Pulmonary involvement in Niemann-Pick disease: case report and literature review

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Niemann-Pick disease type B: an unusual clinical presentation with multiple vertebral fractures

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Functions of lysosomes

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Enzyme therapy in Fabry disease: differential in vivo plasma clearance and metabolic effectiveness of plasma and splenic alpha-galactosidase A isozymes

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Replacement therapy for inherited enzyme deficiency. Use of purified glucocerebrosidase in Gaucher's disease.

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Fabry disease: preclinical studies demonstrate the effectiveness of alpha-galactosidase A replacement in enzyme-deficient mice

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Murine mucopolysaccharidosis VIL: impact of therapies on the phenotype, clinical course, and pathology in a model of a lysosomal storage disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Enzyme replacement and beyond

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Enzyme replacement therapy in mucopolysaccharidosis type I: progress and emerging difficulties

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Receptor mediated binding of two glycosylation forms of N-acetylgalactosamine-4-sulphatase

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Binding, internalization, and degradation of mannose-terminated glucocerebrosidase by macrophages

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Receptor-mediated endocytosis of fibroblast beta-glucuronidase by peritoneal macrophages

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Is movement of mannose 6-phosphate-specific receptor triggered by binding of lysosomal enzymes?

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

The mannose receptor is a pattern recognition receptor involved in host defense

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Analysis of the lung pathology and alveolar macrophage function in the acid sphingomyelinase--deficient mouse model of Niemann-Pick disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Characterization of human acid sphingomyelinase purified from the media of overexpressing Chinese hamster ovary cells

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Acid sphingomyelinase deficient mice: a model of types A and B Niemann–Pick disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

A fluorescence-based, high-performance liquid chromatographic assay to determine acid sphingomyelinase activity and diagnose types A and B Niemann-Pick disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Purification and immunological characterization of the rat liver insulin-like growth factor-II receptor

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Purification and characterization of the D-mannose receptor from J774 mouse macrophage cells

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Lectin-specific targeting of lysosomal enzymes to reticuloendothelial cells

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Mannose 6-phosphate receptor independent targeting of lysosomal enzymes (a mini-review).

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Ligand recognition by purified human mannose receptor

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Biodistribution, kinetics, and efficacy of highly phosphorylated and non-phosphorylated beta-glucuronidase in the murine model of mucopolysaccharidosis VII.

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Replacement Therapy for Inherited Enzyme Deficiency

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Replacement therapy for inherited enzyme deficiency--macrophage-targeted glucocerebrosidase for Gaucher's disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Receptor-mediated pinocytosis of mannose glycoconjugates by macrophages: characterization and evidence for receptor recycling

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Infusion of recombinant human acid sphingomyelinase into niemann-pick disease mice leads to visceral, but not neurological, correction of the pathophysiology

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309465200

21 January 2018

Identifiers

10.1074/JBC.M309465200

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

release_opns323jcradfp2atqxuuybp6i

1 reference

https://api.fatcat.wiki/v0/release/opns323jcradfp2atqxuuybp6i

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PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

2 September 2017

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